Amelogenesis imperfecta	Autosomal recessive hereditary disorder	Hereditary metabolic disease	Hereditary nephropathy	Nephrocalcinosis	Renal failure syndrome
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Enamel-renal syndrome (disorder)
	Enamel-renal syndrome
	Amelogenesis imperfecta and nephrocalcinosis Enamel renal syndrome McGibbon Lubinsky syndrome Amelogenesis imperfecta, nephrocalcinosis and impaired renal concentration
	amelogenesis imperfecta met nefrocalcinose
	enamel-renal syndrome amelogenesis imperfecta type IG

Id	109477002
Status	Primitive

Associated morphology	Pathologic calcification
Finding site	Kidney structure

Associated morphology	Morphologically abnormal structure
Finding site	Enamel structure
Occurrence	Congenital
Pathological process	Pathological developmental process

Has interpretation	Impaired
Interprets	Measurement of renal function

ICD-10 complex map reference set

Target	K00.5
Rule	TRUE
Advice	ALWAYS K00.5
Correlation	SNOMED CT source code to target map code correlation not specified

Target	E83.5
Rule	TRUE
Advice	ALWAYS E83.5
Correlation	SNOMED CT source code to target map code correlation not specified

Target	N29.8
Rule	TRUE
Advice	ALWAYS N29.8 \| THIS CODE MAY BE USED IN THE PRIMARY POSITION WHEN THE MANIFESTATION IS THE PRIMARY FOCUS OF CARE
Correlation	SNOMED CT source code to target map code correlation not specified