Autosomal dominant hereditary disorder	Cardiovascular system hereditary disorder	Cerebral amyloid angiopathy	Chronic disease of cardiovascular system	Chronic organic mental disorder	Degenerative brain disorder	Dementia	Hereditary amyloidosis	Hereditary degenerative disease of central nervous system	Intracerebral vascular finding	Vascular degeneration
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Integral membrane protein 2B related amyloidosis (disorder)
	ITM2B-related amyloidosis
	ITM2B amyloidosis Integral membrane protein 2B related amyloidosis ITM2B-related cerebral amyloid angiopathy
	A rare neurodegenerative disease with characteristics of progressive dementia and ataxia, widespread cerebral amyloid angiopathy and parenchymal amyloid deposition. Two subtypes have been identified, ABri amyloidosis and ADan amyloidosis.
	ITM2B-gerelateerde amyloïdose
	ITM2B-gerelateerde cerebrale amyloïdangiopathie ITM2B-gerelateerde amyloïdstapelingsziekte 'integral membrane protein 2B'-gerelateerde amyloïdose

Id	1187126002
Status	Primitive

Clinical course

Has interpretation	Impaired
Interprets	Cognitive functions

Associated morphology	Amyloid deposition
Finding site	Vascular structure within brain

Associated morphology	Amyloid deposition
Finding site	Structure of parenchyma of brain

ICD-10 complex map reference set

Target	E85.4
Rule	TRUE
Advice	ALWAYS E85.4
Correlation	SNOMED CT source code to target map code correlation not specified

Target	I68.0
Rule	TRUE
Advice	ALWAYS I68.0 \| POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION \| THIS CODE MAY BE USED IN THE PRIMARY POSITION WHEN THE MANIFESTATION IS THE PRIMARY FOCUS OF CARE
Correlation	SNOMED CT source code to target map code correlation not specified

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ABri amyloidosis

ADan amyloidosis