Autosomal recessive hereditary disorder
Combined immunodeficiency disease
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Primary immunodeficiency with multifaceted aberrant lymphoid immunity (disorder)
Primary immunodeficiency with multifaceted aberrant lymphoid immunity
NF-kappa-B-inducing kinase deficiency
NIK deficiency
A rare genetic primary combined T and B cell immunodeficiency with characteristics of recurrent, severe viral and bacterial infections. Immunologic findings include decreased immunoglobulin levels, decreased numbers of B and NK cells, reduced relative CD19+ B cells in peripheral blood, impaired memory responses to viral infections and defective antigen-specific T-cell proliferation.
Id1197478005
StatusPrimitive
Pathological processAbnormal immune process
ICD-10 complex map reference set
TargetD81.8
RuleTRUE
AdviceALWAYS D81.8 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified