Acute digestive system disorder
Acute hepatic failure
Autosomal recessive hereditary disorder
Chronic liver disease
Digestive system hereditary disorder
Recurrent disease
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Fever-associated acute infantile liver failure syndrome (disorder)
Fever-associated acute infantile liver failure syndrome
A rare genetic parenchymatous liver disease with characteristics of infantile or early childhood onset of recurrent episodes of acute liver failure precipitated by a febrile illness. During the life-threatening episodes, patients present with vomiting, lethargy, jaundice as well as elevated levels of liver enzymes and coagulopathy. There is usually complete recovery between the episodes with conservative treatment.
Id1208726006
StatusPrimitive
Clinical courseRecurrent acute
AfterFever
Finding siteStructure of parenchyma of liver
OccurrenceInfancy
ICD-10 complex map reference set
TargetK72.0
RuleTRUE
AdviceALWAYS K72.0 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified