Autosomal dominant hereditary disorder
Carcinoid tumor of small intestine
Digestive system hereditary disorder
Gastrointestinal hormone-secreting endocrine tumor
Hereditary cancer-predisposing syndrome
Malignant tumor of small intestine
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Hereditary malignant neuroendocrine neoplasm of small intestine (disorder)
Hereditary malignant neuroendocrine neoplasm of small intestine
Hereditary malignant neuroendocrine tumor of small intestine
Hereditary malignant neuroendocrine tumor of small bowel
A rare inherited cancer-predisposing syndrome characterized by occurrence of multiple synchronous primary carcinoids of the small intestine. Clinical presentation is otherwise indistinguishable from sporadic carcinoids and includes abdominal pain, flushing, and diarrhea, often becoming manifest only after a long asymptomatic period. Most patients present with low grade tumors. Occurrence of pulmonary carcinoids has also been reported.
Id1222643003
StatusPrimitive
Associated morphologyMalignant carcinoid tumor
Finding siteStructure of small intestine
ICD-10 complex map reference set
TargetC17.9
RuleTRUE
AdviceALWAYS C17.9 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE
CorrelationSNOMED CT source code to target map code correlation not specified