Autoimmune disease	Autosomal recessive hereditary disorder	Combined immunodeficiency disease
\|	\|	\|

Autoimmune hemolytic anemia, autoimmune thrombocytopenia, primary immunodeficiency syndrome (disorder)
	Autoimmune hemolytic anemia, autoimmune thrombocytopenia, primary immunodeficiency syndrome
	TPPII-related immunodeficiency, autoimmunity and neurodevelopmental delay with impaired glycolysis and lysosomal expansion disease Evans syndrome associated with primary immunodeficiency TRIANGLE (TPPII-related immunodeficiency, autoimmunity, neurodevelopmental delay, impaired glycolysis, lysosomal expansion) disease Tripeptidyl-peptidase II deficiency TPPII (tripeptidyl-peptidase II) deficiency
	A rare genetic immune disease with characteristics of infantile or childhood onset of combined immunodeficiency with recurrent viral, bacterial, and fungal infections, severe autoimmunity mainly manifesting as antibody-mediated destruction of red blood cells, platelets and neutrophils and mild to moderate developmental delay. Laboratory findings include decreased circulating T-, B-, and natural killer cells, and hypergammaglobulinemia.

Id	1222681008
Status	Primitive

Pathological process

Autoimmune process

ICD-10 complex map reference set

Target	D89.8
Rule	TRUE
Advice	ALWAYS D89.8 \| POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
Correlation	SNOMED CT source code to target map code correlation not specified