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Leukocyte chemotactic factor-2 amyloidosis (disorder)
ALECT2 amyloidosis
Leukocyte chemotactic factor-2 amyloidosis
A rare systemic amyloidosis with characteristics of slowly progressive renal disease presenting with proteinuria, hypertension and decreased glomerular filtration rate leading to progressive renal failure. Histology reveals amyloid deposits of leukocyte chemotactic factor-2 protein in the renal cortical interstitium, tubular basement membranes, glomeruli and the vessel walls. Extra-renal deposits can be seen in the liver, lungs, spleen and adrenal glands.
Id1228881003
StatusPrimitive
Clinical courseProgressive
Associated morphologyAmyloid deposition
Finding siteKidney structure
ICD-10 complex map reference set
TargetE85.8
RuleTRUE
AdviceALWAYS E85.8 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified