Indolent systemic mastocytosis
Myeloproliferative disorder
Neoplasm affecting hematopoietic structure
Neoplasm of bone marrow
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Isolated bone marrow mastocytosis (disorder)
Isolated bone marrow mastocytosis
A rare subtype of indolent systemic mastocytosis with characteristics of isolated bone marrow involvement without skin lesions, low burden of neoplastic mast cells and often normal or near normal serum tryptase levels. The KIT D816V mutation is present in the majority of cases.
Id1231735008
StatusPrimitive
Associated morphologyBone marrow mastocytosis
Finding siteBone marrow structure
ICD-10 complex map reference set
TargetD47.0
RuleTRUE
AdviceALWAYS D47.0 | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE
CorrelationSNOMED CT source code to target map code correlation not specified