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Deficiency of oxoglutarate dehydrogenase (lipoamide) (disorder)
Deficiency of oxoglutarate dehydrogenase (lipoamide)
Deficiency of oxoglutarate decarboxylase
Deficiency of alpha-ketoglutaric dehydrogenase
deficiƫntie van 2-ketoglutaarzuurdehydrogenase
2-ketoglutaarzuurdehydrogenasedeficiƫntie
Id124162009
StatusPrimitive
DHD Diagnosis thesaurus reference set
ICD-10 complex map reference set
TargetE88.0
RuleTRUE
AdviceALWAYS E88.0 | POSSIBLE REQUIREMENT FOR AN EXTERNAL CAUSE CODE
CorrelationSNOMED CT source code to target map code correlation not specified