Autosomal recessive hereditary disorder	Congenital anomaly of peripheral nerve	Developmental hereditary disorder	Digestive system hereditary disorder	Disorder of sympathetic nervous system	Hirschsprung's disease	Inherited autonomic nervous system disorder	Nerve plexus disorder
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Total intestinal aganglionosis (disorder)
	Total intestinal aganglionosis
	ziekte van Hirschsprung van volledig intestinum
	compleet aganglionair megacolon van darmkanaal totale aganglionose van darm megacolon congenitum van volledig intestinum

Id	204745000
Status	Primitive

Associated morphology	Hypertrophy
Finding site	Large intestine part
Occurrence	Congenital
Pathological process	Pathological developmental process

Associated morphology	Morphologically abnormal structure
Finding site	Superior mesenteric plexus structure
Occurrence	Congenital
Pathological process	Pathological developmental process

Associated morphology	Morphologically abnormal structure
Finding site	Structure of peripheral part of autonomic nervous system
Occurrence	Congenital
Pathological process	Pathological developmental process

Associated morphology	Dilatation
Finding site	Large intestine part
Occurrence	Congenital
Pathological process	Pathological developmental process

ICD-10 complex map reference set

Target	Q43.1
Rule	TRUE
Advice	ALWAYS Q43.1
Correlation	SNOMED CT source code to target map code correlation not specified