Organic acid metabolism disorder marker
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Branched chain organic acid disorder marker (substance)
Branched chain organic acid disorder marker
Id
259457004
Status
Primitive
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2-methyl-3-hydroxybutyrate
2-methylacetoacetate
3-hydroxy-3-methyl-glutarate
3-methylglutaconate
3-methylglutarate
Acetyl-coenzyme A C-acetyltransferase
Branched chain ketoacid decarboxylase
Isovaleric acid
Isovaleryl-CoA dehydrogenase
Mevalonate