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Congenital total lipodystrophy (disorder)
Congenital generalized lipodystrophy
Congenital total lipodystrophy
Seip's syndrome
Beradinelli-Seip syndrome
Total lipoatrophy
Lawrence-Seip syndrome
Berardinelli's syndrome
Lipoatrophic diabetes mellitus
Berardinelli-Seip congenital lipodystrophy
congenitale gegeneraliseerde lipodystrofie
Berardinelli-Seip-syndroom
syndroom van Berardinelli-Seip
congenitale totale lipodystrofie
Id284449005
StatusPrimitive
Associated morphologyDystrophy
Finding siteSubcutaneous fatty tissue
OccurrenceCongenital
DHD Diagnosis thesaurus reference set
ICD-10 complex map reference set
TargetE88.1
RuleTRUE
AdviceALWAYS E88.1 | POSSIBLE REQUIREMENT FOR AN EXTERNAL CAUSE CODE
CorrelationSNOMED CT source code to target map code correlation not specified
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