Congenital total lipodystrophy (disorder) | | Congenital generalized lipodystrophy | | Congenital total lipodystrophy Seip's syndrome Beradinelli-Seip syndrome Total lipoatrophy Lawrence-Seip syndrome Berardinelli's syndrome Lipoatrophic diabetes mellitus Berardinelli-Seip congenital lipodystrophy
| | congenitale gegeneraliseerde lipodystrofie | | Berardinelli-Seip-syndroom syndroom van Berardinelli-Seip congenitale totale lipodystrofie
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| Id | 284449005 | Status | Primitive |
DHD Diagnosis thesaurus reference set |
ICD-10 complex map reference set | Target | E88.1 | Rule | TRUE | Advice | ALWAYS E88.1 | POSSIBLE REQUIREMENT FOR AN EXTERNAL CAUSE CODE | Correlation | SNOMED CT source code to target map code correlation not specified |
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