Autosomal dominant hereditary disorder	Biliary tract dysplasia	Congenital anomaly of bile ducts	Congenital anomaly of liver	Congenital dysplasia	Developmental hereditary disorder	Digestive system hereditary disorder	Hereditary cancer-predisposing syndrome	Lesion of liver	Multiple system malformation syndrome
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Arteriohepatic dysplasia (disorder)
	Arteriohepatic dysplasia
	Watson-Alagille syndrome Alagille syndrome
	Alagille-syndroom
	syndroom van Alagille arteriohepatische dysplasie
	syndroom van Alagille
	Erfelijke aandoening waarbij een tekort aan galgangetjes of vernauwing van galgangetjes in de lever leidt tot geelzucht, hevige jeuk en onderhuidse vetbultjes; soms leidend tot afwijkingen in gezicht, hart, bloedvaten en wervelkolom.

Id	31742004
Status	Primitive

Associated morphology	Dysplasia
Finding site	Intrahepatic biliary tract structure
Occurrence	Congenital
Pathological process	Pathological developmental process

PALGA thesaurus simple reference set for pathology

DHD Diagnosis thesaurus reference set

ICD-10 complex map reference set

Target	Q44.7
Rule	TRUE
Advice	ALWAYS Q44.7
Correlation	SNOMED CT source code to target map code correlation not specified