Cardiovascular system hereditary disorder	Hereditary disorder of the integument	Hereditary red blood cell disorder	Inherited platelet disorder	Thrombotic thrombocytopenic purpura
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Upshaw-Schulman syndrome (disorder)
	Upshaw-Schulman syndrome
	Familial TTP/HUS Familial thrombotic thrombocytopenic purpura / hemolytic uremic syndrome
	syndroom van familiaire trombotische trombocytopenische purpura en hemolytische uremie
	syndroom van Upshaw-Schulman Upshaw-Schulman-syndroom familiaire trombotische trombocytopenische purpura en trombotische microangiopathie familiaire TTP-TMA familiaire TTP-HUS

Id	373420004
Status	Primitive

Associated morphology	Thrombus
Finding site	Structure of capillary blood vessel

Associated morphology

Has interpretation	Below reference range
Interprets	Measurement of total hemoglobin concentration

Has interpretation	Below reference range
Interprets	Red blood cell count

Associated morphology	Purpura
Finding site	Skin structure
Occurrence	Period of life between birth and death

Finding site

Has interpretation	Present
Interprets	Hemolysis

Has interpretation	Abnormal
Interprets	Hemostatic function

Has interpretation	Below reference range
Interprets	Platelet count

ICD-10 complex map reference set

Target	M31.1
Rule	TRUE
Advice	ALWAYS M31.1
Correlation	SNOMED CT source code to target map code correlation not specified