Congenital skin contracture	Developmental hereditary disorder	Laminopathy with premature aging
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Lethal tight skin contracture syndrome (disorder)
	Lethal tight skin contracture syndrome
	Infantile restrictive dermopathy
	restrictieve dermopathie

Id	400128006
Status	Primitive

Associated morphology	Contracture
Finding site	Skin structure
Occurrence	Congenital
Pathological process	Pathological developmental process

DHD Diagnosis thesaurus reference set

ICD-10 complex map reference set

Target	Q82.8
Rule	TRUE
Advice	ALWAYS Q82.8
Correlation	SNOMED CT source code to target map code correlation not specified