Hereditary cancer-predisposing syndrome	Hereditary disorder of nervous system	Hereditary disorder of the integument	Neurocutaneous syndrome
\|	\|	\|	\|

Von Hippel-Lindau syndrome (disorder)
	Von Hippel-Lindau syndrome
	Cerebroretinal angiomatosis Lindau' disease Familial cerebello-retinal angiomatosis Lindau's disease VHL (Von Hippel-Lindau) syndrome
	Von Hippel-Lindau-syndroom
	syndroom van Von Hippel-Lindau
	ziekte van Von Hippel-Lindau
	VHL
	VHL; erfelijke aandoening waarbij een verhoogde kans aanwezig is op goed- of kwaadaardige tumoren in onder meer de ogen, kleine hersenen, alvleesklier en (bij)nieren.

Id	46659004
Status	Primitive

Associated morphology	Neoplasm
Finding site	Structure of nervous system
Occurrence	Congenital

Associated morphology	Neoplasm
Finding site	Skin structure
Occurrence	Congenital

PALGA thesaurus simple reference set for pathology

General Practice / Family Practice reference set

DHD Diagnosis thesaurus reference set

ICD-10 complex map reference set

Target	Q85.8
Rule	TRUE
Advice	ALWAYS Q85.8
Correlation	SNOMED CT source code to target map code correlation not specified

|

Pre-existing Von Hippel-Lindau syndrome in pregnancy