Inborn error of metabolism	Non-amino organic acidemia AND/OR aciduria	Specific enzyme deficiency
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Deficiency of acetyl-coenzyme A carboxylase (disorder)
	Acetyl-CoA carboxylase deficiency
	Deficiency of acetyl-CoA carboxylase Deficiency of acetyl-coenzyme A carboxylase
	deficiëntie van acetyl-co-enzym-A-carboxylase
	deficiëntie van acetyl-CoA-carboxylase acetyl-CoA-carboxylasedeficiëntie acetyl-co-enzym-A-carboxylasedeficiëntie

Id	4920001
Status	Primitive

Occurrence

Congenital

ICD-10 complex map reference set

Target	E71.3
Rule	TRUE
Advice	ALWAYS E71.3
Correlation	SNOMED CT source code to target map code correlation not specified