Autosomal recessive hereditary disorder	Chronic metabolic disorder	Cirrhosis of liver	Digestive system hereditary disorder	Disorder of biliary tract	Hereditary metabolic disease	Intrahepatic cholestasis	Metabolic and genetic disorder affecting the liver
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North American Indian childhood cirrhosis (disorder)
	North American Indian childhood cirrhosis
	NAIC - North American Indian childhood cirrhosis
	Severe autosomal recessive intrahepatic cholestasis described in aboriginal children from northwestern Quebec. First manifestation as neonatal jaundice, progresses to periportal fibrosis and cirrhosis.
	hereditaire levercirrose op kinderleeftijd bij Noord-Amerikaanse indianen
	erfelijke cirrose op kinderleeftijd bij Noord-Amerikaanse indianen hereditaire cirrose op kinderleeftijd bij Noord-Amerikaanse indianen

Id	699189004
Status	Primitive

Associated morphology	Chronic fibrosis
Finding site	Liver structure
Occurrence	Childhood

Associated morphology	Nodular regeneration
Finding site	Liver structure
Occurrence	Childhood

Finding site	Biliary tract structure
Occurrence	Childhood

Clinical course

ICD-10 complex map reference set

Target	K74.6
Rule	TRUE
Advice	ALWAYS K74.6
Correlation	SNOMED CT source code to target map code correlation not specified