Autosomal recessive hereditary disorder	Congenital malformation of genital organs	Developmental hereditary disorder	Multiple system malformation syndrome	Polydactyly	Reproductive system hereditary disorder
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Hydrometrocolpos, postaxial polydactyly, and congenital heart malformation (disorder)
	McKusick Kaufman syndrome
	Hydrometrocolpos, postaxial polydactyly, and congenital heart malformation
	syndroom van hydrometrocolpos, postaxiale polydactylie en congenitale hartmalformatie
	syndroom van Kaufman-McKusick syndroom van McKusick-Kaufman syndroom van hydrometrocolpos en postaxiale polydactylie

Id	702407009
Status	Primitive

Associated morphology	Morphologically abnormal structure
Finding site	Genital structure
Occurrence	Congenital
Pathological process	Pathological developmental process

Associated morphology	Supernumerary structure
Finding site	Digit structure
Occurrence	Congenital
Pathological process	Pathological developmental process

DHD Diagnosis thesaurus reference set

ICD-10 complex map reference set

Target	Q87.8
Rule	TRUE
Advice	ALWAYS Q87.8
Correlation	SNOMED CT source code to target map code correlation not specified