Auditory system hereditary disorder	Autosomal recessive hereditary disorder	Chronic disease of ear	Congenital fusion of ossicles of ear	Congenital hearing disorder	Developmental hereditary disorder
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Progressive deafness with stapes fixation (disorder)
	Progressive deafness with stapes fixation
	Stapedo-vestibular ankylosis Thies Reis syndrome
	A hearing loss condition that appears as a consequence of annular ligament destruction followed by excessive connective tissue production during the healing process. This condition is mainly observed in otosclerosis, but is also found in chronic otitis media with tympanosclerosis, and other rare bone diseases such as Paget's disease and osteogenesis imperfecta (Lobstein disease).
	progressieve doofheid met stapesfixatie
	progressieve doofheid met stijgbeugelfixatie syndroom van Thies-Reis stapedovestibulaire ankylose Thies-Reis-syndroom

Id	715529009
Status	Primitive

Clinical course

Interprets

Associated morphology	Fusion
Finding site	Stapes structure
Occurrence	Congenital
Pathological process	Pathological developmental process

DHD Diagnosis thesaurus reference set

ICD-10 complex map reference set

Target	H74.3
Rule	TRUE
Advice	ALWAYS H74.3 \| POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
Correlation	SNOMED CT source code to target map code correlation not specified