Posterior cortical atrophy syndrome (disorder) | | Posterior cortical atrophy syndrome | | Benson syndrome Posterior cortical atrophy
| | A rare progressive neurodegenerative disorder with typical onset between 50 and 65 years of age. Manifestation is of progressive impairment of higher visual processing skills and other posterior cortical functions without any evidence of ocular abnormalities. Prevalence is unknown, largely due to the lack of awareness of the syndrome and the inaccurate terminology referring to it. Alzheimer's disease is the most common underlying pathology, but cases attributable to Dementia with Lewy Bodies, corticobasal degeneration or prion disease have also been reported. | | posterieure corticale atrofie | | syndroom van Benson PCA
| | posterieure corticale atrofie | | PCA; zeldzame vorm van dementie waarbij het achterste deel van de hersenen wordt aangetast, dat gebruikt wordt voor visuele waarnemingen; door deze vorm van dementie ziet iemand dingen anders dan ze zijn of ziet ze helemaal niet. |
| Id | 715574002 | Status | Primitive |
DHD Diagnosis thesaurus reference set |
ICD-10 complex map reference set | Target | G31.1 | Rule | TRUE | Advice | ALWAYS G31.1 | Correlation | SNOMED CT source code to target map code correlation not specified |
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