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Periodic fever and aphthous stomatitis with pharyngitis and cervical lymphadenitis syndrome (disorder)
PFAPA syndrome
Marshall syndrome with periodic fever
Periodic fever and aphthous stomatitis with pharyngitis and cervical lymphadenitis syndrome
An auto inflammatory syndrome with characteristics of recurrent febrile episodes associated with aphthous stomatitis, pharyngitis and cervical adenitis. Usually presents during early childhood with recurrent episodes of fever during which children appear very ill. Aphthous stomatitis presents with relatively painless small, round and shallow lesions on the tongue and oral mucosa that recover completely in 10-14 days. Most patients present with tonsillitis, occasionally with white exudates and a general pharyngitis. Episodes recur every 3-5 weeks, often in a predictable fashion with patients describing a mild malaise the day before recurrence. An idiopathic inflammatory condition.
syndroom van periodieke koorts en stomatitis aphthosa met faryngitis en cervicale lymfadenitis
'periodic fever and aphthous stomatitis with pharyngitis and adenitis'-syndroom
'periodic fever and aphthous stomatitis with pharyngitis and cervical lymphadenitis'-syndroom
PFAPA-syndroom
Id717231003
StatusPrimitive
Associated morphologyAphtha
Finding siteOral mucous membrane structure
Associated morphologyInflammatory morphology
Finding sitePharyngeal structure
Clinical courseRecurrent
Has interpretationAbove reference range
InterpretsBody temperature
DHD Diagnosis thesaurus reference set
ICD-10 complex map reference set
TargetE85.0
RuleTRUE
AdviceALWAYS E85.0
CorrelationSNOMED CT source code to target map code correlation not specified
TargetI88.9
RuleTRUE
AdviceALWAYS I88.9
CorrelationSNOMED CT source code to target map code correlation not specified
TargetK12.0
RuleTRUE
AdviceALWAYS K12.0
CorrelationSNOMED CT source code to target map code correlation not specified
TargetJ02.9
RuleTRUE
AdviceALWAYS J02.9
CorrelationSNOMED CT source code to target map code correlation not specified