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Double uterus, hemivagina, renal agenesis syndrome (disorder)
Double uterus, hemivagina, renal agenesis syndrome
Double uterus and obstructed hemivagina syndrome
Herlyn Werner syndrome
Obstructed hemivagina and ipsilateral renal anomaly
Wunderlich syndrome
A rare congenital urogenital anomaly characterized by the presence of double uterus (didelphys, bicornuate or septum-complete or partial), unilateral cervico-vaginal obstruction and ipsilateral renal anomalies (renal agenesis and/or other urinary tract anomalies). Patients are usually diagnosed at puberty after menarche due to recurrent severe dysmenorrhea, chronic pelvic pain, excessive foul smelling mucopurulent discharge, spotting and intermenstrual bleeding (depending on the existence of uterine or vaginal communications). Fever, dyspareunia, and a palpable abdominal, pelvic or vaginal mass (mucocolpos or pyocolpos) may also be present.
syndroom van dubbele uterus, hemivagina en renale agenesie
'obstructed hemivagina and ipsilateral renal anomaly'-syndroom
syndroom van Herlyn-Werner-Wunderlich
HWW-syndroom
Herlyn-Werner-Wunderlich-syndroom
syndroom van uterus didelphys, bicornis of bilocularis, geobstrueerde hemivagina en ipsilaterale nieragenesie
OHVIRA-syndroom
Id722431007
StatusPrimitive
Associated morphologyMorphologically abnormal structure
Finding siteKidney structure
OccurrenceCongenital
Pathological processPathological developmental process
DHD Diagnosis thesaurus reference set
ICD-10 complex map reference set
TargetQ51.1
RuleTRUE
AdviceALWAYS Q51.1 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified
TargetQ60.0
RuleTRUE
AdviceALWAYS Q60.0
CorrelationSNOMED CT source code to target map code correlation not specified