Double uterus, hemivagina, renal agenesis syndrome (disorder) | | Double uterus, hemivagina, renal agenesis syndrome | | Double uterus and obstructed hemivagina syndrome Herlyn Werner syndrome Obstructed hemivagina and ipsilateral renal anomaly Wunderlich syndrome
| | A rare congenital urogenital anomaly characterized by the presence of double uterus (didelphys, bicornuate or septum-complete or partial), unilateral cervico-vaginal obstruction and ipsilateral renal anomalies (renal agenesis and/or other urinary tract anomalies). Patients are usually diagnosed at puberty after menarche due to recurrent severe dysmenorrhea, chronic pelvic pain, excessive foul smelling mucopurulent discharge, spotting and intermenstrual bleeding (depending on the existence of uterine or vaginal communications). Fever, dyspareunia, and a palpable abdominal, pelvic or vaginal mass (mucocolpos or pyocolpos) may also be present. | | syndroom van dubbele uterus, hemivagina en renale agenesie | | 'obstructed hemivagina and ipsilateral renal anomaly'-syndroom syndroom van Herlyn-Werner-Wunderlich HWW-syndroom Herlyn-Werner-Wunderlich-syndroom syndroom van uterus didelphys, bicornis of bilocularis, geobstrueerde hemivagina en ipsilaterale nieragenesie OHVIRA-syndroom
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| Id | 722431007 | Status | Primitive |
DHD Diagnosis thesaurus reference set |
ICD-10 complex map reference set | Target | Q51.1 | Rule | TRUE | Advice | ALWAYS Q51.1 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | Correlation | SNOMED CT source code to target map code correlation not specified |
Target | Q60.0 | Rule | TRUE | Advice | ALWAYS Q60.0 | Correlation | SNOMED CT source code to target map code correlation not specified |
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