Bone marrow disorder	Chronic liver disease	Connective tissue hereditary disorder	Digestive system hereditary disorder	Idiopathic pulmonary fibrosis	Nodular regenerative hyperplasia of liver
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Pulmonary fibrosis, hepatic hyperplasia, bone marrow hypoplasia syndrome (disorder)
	Pulmonary fibrosis, hepatic hyperplasia, bone marrow hypoplasia syndrome
	Trimorphic syndrome
	A rare disease with three inherited morbidities; idiopathic pulmonary fibrosis, hepatic nodular regenerative hyperplasia leading to portal hypertension and thrombocytopenia due to bone marrow hypoplasia. The condition is associated with 100% mortality.
	syndroom van longfibrose, leverhyperplasie en beenmerghypoplasie

Id	723829000
Status	Primitive

Associated morphology	Nodular regenerative hyperplasia
Finding site	Liver structure

Associated morphology	Hypoplasia
Finding site	Bone marrow structure

Associated morphology	Fibrosis
Finding site	Lung structure

Clinical course

Associated morphology	Inflammation and consolidation
Finding site	Structure of interstitial tissue of lung

DHD Diagnosis thesaurus reference set

ICD-10 complex map reference set

Target	J84.1
Rule	TRUE
Advice	ALWAYS J84.1 \| POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
Correlation	SNOMED CT source code to target map code correlation not specified

Target	Q44.7
Rule	TRUE
Advice	ALWAYS Q44.7
Correlation	SNOMED CT source code to target map code correlation not specified

Target	D61.9
Rule	TRUE
Advice	ALWAYS D61.9
Correlation	SNOMED CT source code to target map code correlation not specified