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Hereditary anetoderma (disorder)
Hereditary anetoderma
Hereditary macular atrophy
An extremely rare genetic skin disease characterized by loss of elastin tissue leading to localized areas of flaccid skin and a family history of the disorder.
hereditaire anetodermie
erfelijke atrophia cutis maculosa
erfelijke maculaire atrofie
erfelijke dermatitis atrophicans maculosa
Id733467001
StatusPrimitive
Associated morphologyFocal atrophy
Finding siteSkin structure
OccurrenceCongenital
DHD Diagnosis thesaurus reference set
ICD-10 complex map reference set
TargetL90.8
RuleTRUE
AdviceALWAYS L90.8
CorrelationSNOMED CT source code to target map code correlation not specified