Chronic disease of skin
Non-Langerhans cell histiocytic dermatosis
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Progressive nodular histiocytosis (disorder)
Progressive nodular histiocytosis
A rare normolipemic non-Langerhans cell histiocytosis characterized by progressive growth of multiple to disseminated asymptomatic skin lesions that range in appearance from yellow plaques to coalescence-prone red-brown papules, nodules and pedunculated tumors up to 5 cm in size, located typically on the face, trunk and extremities (and rarely on conjunctiva and mucous membranes). Characteristic microscopic findings include a storiform spindle cell infiltrate in the deep dermis with xanthoma macrophages and some Touton cells in the upper dermis. It is usually not associated with systemic disease.
progressieve nodulaire histiocytose
Id765141005
StatusPrimitive
Associated morphologyHistiocytic proliferation
Finding siteDermis structure
Clinical courseProgressive
DHD Diagnosis thesaurus reference set
ICD-10 complex map reference set
TargetD76.3
RuleTRUE
AdviceALWAYS D76.3
CorrelationSNOMED CT source code to target map code correlation not specified