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Dentin dysplasia with sclerotic bone syndrome (disorder)
Dentin dysplasia with sclerotic bone syndrome
Dentin dysplasia, sclerotic bones syndrome
A rare genetic odontologic disease with characteristics of the clinical, radiographic and histologic features of dentin dysplasia and osteosclerosis of all long bones, with heavy cortical bone and narrowed or occluded marrow spaces. There have been no further descriptions in the literature since 1977.
syndroom van dentinedysplasie en osteosclerose
Id770943008
StatusPrimitive
Associated morphologyBony sclerosis
Finding siteBone structure
OccurrenceCongenital
Pathological processPathological developmental process
Associated morphologyDysplasia
Finding siteDentin structure
OccurrenceCongenital
Pathological processPathological developmental process
Clinical courseProgressive
DHD Diagnosis thesaurus reference set
ICD-10 complex map reference set
TargetK00.5
RuleTRUE
AdviceALWAYS K00.5
CorrelationSNOMED CT source code to target map code correlation not specified
TargetQ77.4
RuleTRUE
AdviceALWAYS Q77.4
CorrelationSNOMED CT source code to target map code correlation not specified