Congenital anomaly of cerebrum	Congenital anosmia	Congenital brain aplasia	Hemianencephaly
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Isolated arhinencephaly (disorder)
	Isolated arhinencephaly
	A rare non-syndromic central nervous system malformation defined by the agenesis of the olfactory bulbs and tracts and with characteristics of complete congenital anosmia.
	geïsoleerde arinencefalie

Id	771147003
Status	Primitive

Associated morphology	Agenesis
Finding site	Entire olfactory bulb
Occurrence	Congenital
Pathological process	Pathological developmental process

Associated morphology	Agenesis
Finding site	Entire olfactory tract
Occurrence	Congenital
Pathological process	Pathological developmental process

Has interpretation	Absent
Interprets	Sense of smell, function

DHD Diagnosis thesaurus reference set

ICD-10 complex map reference set

Target	Q04.1
Rule	TRUE
Advice	ALWAYS Q04.1
Correlation	SNOMED CT source code to target map code correlation not specified