Infantile onset panniculitis with uveitis and systemic granulomatosis (disorder)
Infantile onset panniculitis with uveitis and systemic granulomatosis
A rare granulomatous autoinflammatory disease with characteristics of infantile-onset, widespread, chronic, recurrent, progressive, lobular panniculitis associated with panuveitis, arthritis and severe systemic granulomatous inflammation.
panniculitis met uveïtis en systemische granulomatose beginnend op zuigelingenleeftijd