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Infantile onset panniculitis with uveitis and systemic granulomatosis (disorder)
Infantile onset panniculitis with uveitis and systemic granulomatosis
A rare granulomatous autoinflammatory disease with characteristics of infantile-onset, widespread, chronic, recurrent, progressive, lobular panniculitis associated with panuveitis, arthritis and severe systemic granulomatous inflammation.
panniculitis met uveïtis en systemische granulomatose beginnend op zuigelingenleeftijd
Id773328002
StatusPrimitive
Associated morphologyGranulomatosis
OccurrenceInfancy
Clinical courseChronic
Associated morphologyInflammatory morphology
Finding siteSubcutaneous fatty tissue
OccurrenceInfancy
Associated morphologyInflammatory morphology
Finding siteUveal tract structure
OccurrenceInfancy
Associated morphologyInflammatory morphology
Finding siteStructure of immune system
Pathological processAbnormal immune process
DHD Diagnosis thesaurus reference set
ICD-10 complex map reference set
TargetM08.89
RuleTRUE
AdviceALWAYS M08.89 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified