Angiolipoma
Autosomal recessive hereditary disorder
Familial neoplastic disease
Hereditary disorder of the integument
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Familial angiolipomatosis (disorder)
Familial angiolipomatosis
A rare genetic subcutaneous tissue disorder with the presence of benign usually multiple subcutaneous tumors. The tumors are composed of adipose tissue and blood vessels typically manifesting as yellow firm circumscribed 1-4 cm in diameter tumors located in the arms, legs and trunk with deep extension of the lesions between muscles, tendons and joint capsules (without infiltration of these structures) in several members of a single family. Tumors may be tender or mildly painful when palpated and do not regress spontaneously.
familiaire angiolipomatose
familiale angiolipomatose
Id774066000
StatusPrimitive
Associated morphologyAngiolipoma
Finding siteSubcutaneous tissue structure
DHD Diagnosis thesaurus reference set
ICD-10 complex map reference set
TargetD17.9
RuleTRUE
AdviceALWAYS D17.9 | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE
CorrelationSNOMED CT source code to target map code correlation not specified