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Neonatal dermatomyositis (disorder)
Neonatal dermatomyositis
A very rare secondary neonatal autoimmune disease characterized by generalized weakness, severe hypotonia, absent or reduced deep tendon reflexes and highly elevated serum creatine kinase levels presenting in the neonatal period. Perifascicular atrophy in the presence of a diffuse perivascular inflammatory cell exudate is observed on muscle biopsy.
neonatale dermatomyositis
dermatomyositis bij pasgeborene
dermatomyositis bij neonaat
Id774082004
StatusPrimitive
Associated morphologyInflammatory morphology
Finding siteSkin structure
OccurrenceNeonatal
Pathological processAutoimmune process
Associated morphologyInflammatory morphology
Finding siteSkeletal muscle structure
OccurrenceNeonatal
Pathological processAutoimmune process
DHD Diagnosis thesaurus reference set
ICD-10 complex map reference set
TargetM33.1
RuleTRUE
AdviceALWAYS M33.1 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified