Aplasia cutis congenita	Congenital anomaly of central nervous system	Congenital hamartoma of skin	Multiple system malformation syndrome	Sebaceous nevus
\|	\|	\|	\|	\|

Sebaceous nevus, central nervous system malformations, aplasia cutis congenita, limbal dermoid, pigmented nevus syndrome (disorder)
	SCALP syndrome
	Sebaceous nevus, central nervous system malformations, aplasia cutis congenita, limbal dermoid, pigmented nevus syndrome
	A rare skin disease characterized by the association of sebaceous nevus and aplasia cutis congenita (usually on the scalp and face) in conjunction with limbal dermoid of the eye, a giant congenital melanocytic nevus and variable central nervous system abnormalities including seizures, hydrocephalus, neurocutaneous melanosis, arachnoid cysts, and diffuse unilateral hemisphere enlargement.
	syndroom van naevus sebaceus, malformaties van centraal zenuwstelsel, aplasia cutis congenita, limbale dermoïdcyste en naevus pigmentosus
	SCALP-syndroom syndroom van talgkliernaevus, CZS-malformaties, aplasia cutis congenita, limbaal dermoïd en pigmentvlek

Id	774208009
Status	Primitive

Associated morphology	Epidermal nevus
Finding site	Skin structure
Occurrence	Congenital

Associated morphology	Aplasia
Finding site	Skin part
Occurrence	Congenital
Pathological process	Pathological developmental process

Associated morphology	Morphologically abnormal structure
Finding site	Structure of central nervous system
Occurrence	Congenital
Pathological process	Pathological developmental process

DHD Diagnosis thesaurus reference set

ICD-10 complex map reference set

Target	Q84.8
Rule	TRUE
Advice	ALWAYS Q84.8 \| POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
Correlation	SNOMED CT source code to target map code correlation not specified