Benign neoplasm of nervous system
Neurofibromatosis syndrome
Schwannoma
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Schwannomatosis (disorder)
Schwannomatosis
Neurilemmomatosis
The least frequent form of the rare genetic disorder neurofibromatosis. It is clinically and genetically distinct from Neurofibromatosis type 1 and Neurofibromatosis type 2 and is characterized by the development of multiple schwannomas (nerve sheath tumors), without involvement of the vestibular nerves. The disease develops in adulthood and is often associated with chronic pain. Dysesthesia and paresthesia may also be present. Common localizations include the spine, peripheral nerves and the cranium.
schwannomatose
Id781641005
StatusPrimitive
Associated morphologyNeurofibromatosis
Finding siteStructure of nervous system
OccurrenceCongenital
Associated morphologySchwannoma
Finding siteStructure of nervous system
Associated morphologyNeurofibromatosis
Finding siteSkin structure
OccurrenceCongenital
DHD Diagnosis thesaurus reference set
ICD-10 complex map reference set
TargetQ85.0
RuleTRUE
AdviceALWAYS Q85.0 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified