Idiopathic retinal vasculitis, aneurysms, neuroretinitis syndrome (disorder) | | IRVAN syndrome | | Idiopathic retinal vasculitis, aneurysms, neuroretinitis syndrome IRVAN (idiopathic retinal vasculitis, aneurysms, neuroretinitis) syndrome
| | A rare retinal vasculopathy disease characterized by idiopathic retinal vasculitis (IRV), aneurysmal dilations (A) at arteriolar bifurcations and neuroretinitis (N), which if untreated progresses to peripheral capillary non-perfusion retinal neovascularization and macular exudation, leading to severe bilateral vision loss. | | syndroom van idiopathische retinale vasculitis, aneurysmata en neuroretinitis | | IRVAN-syndroom
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| Id | 783090002 | Status | Primitive |
DHD Diagnosis thesaurus reference set |
ICD-10 complex map reference set | Target | H35.0 | Rule | TRUE | Advice | ALWAYS H35.0 | Correlation | SNOMED CT source code to target map code correlation not specified |
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