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Idiopathic retinal vasculitis, aneurysms, neuroretinitis syndrome (disorder)
IRVAN syndrome
Idiopathic retinal vasculitis, aneurysms, neuroretinitis syndrome
IRVAN (idiopathic retinal vasculitis, aneurysms, neuroretinitis) syndrome
A rare retinal vasculopathy disease characterized by idiopathic retinal vasculitis (IRV), aneurysmal dilations (A) at arteriolar bifurcations and neuroretinitis (N), which if untreated progresses to peripheral capillary non-perfusion retinal neovascularization and macular exudation, leading to severe bilateral vision loss.
syndroom van idiopathische retinale vasculitis, aneurysmata en neuroretinitis
IRVAN-syndroom
Id783090002
StatusPrimitive
Associated morphologyInflammatory morphology
Finding siteOptic disc structure
Associated morphologyAneurysm
Finding siteArterial structure
DHD Diagnosis thesaurus reference set
ICD-10 complex map reference set
TargetH35.0
RuleTRUE
AdviceALWAYS H35.0
CorrelationSNOMED CT source code to target map code correlation not specified