Lymphangiectasis	Lymphatic malformation	Soft tissue lesion
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Congenital lymphangiectasia (disorder)
	Congenital lymphangiectasia
	Congenital lymphangiectasis Congenital lymphangiectases
	congenitale lymfangiëctasie
	aangeboren lymfangiëctasie

Id	788292004
Status	Defined

Associated morphology	Lymphangiectasis
Finding site	Structure of lymphatic vessel
Occurrence	Congenital
Pathological process	Pathological developmental process

ICD-10 complex map reference set

Target	I89.0
Rule	TRUE
Advice	ALWAYS I89.0
Correlation	SNOMED CT source code to target map code correlation not specified

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Aplasia cutis congenita with intestinal lymphangiectasia syndrome

Congenital cutaneous lymphangiectasia

Congenital lymphangiectasia with chylous reflux

Congenital pulmonary lymphangiectasis2

Hennekam syndrome

Persistent Mullerian derivative with lymphangiectasia and polydactyly syndrome