Autosomal recessive hereditary disorder	Digestive system hereditary disorder	Disorder of lipid storage and metabolism	Disorder of lysosomal enzyme	Disorder of pancreas	Hereditary disorder of endocrine system	Malabsorption syndrome
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Pancreatic triacylglycerol lipase deficiency (disorder)
	Pancreatic triacylglycerol lipase deficiency
	Isolated lipase deficiency Congenital absence of pancreatic lipase Congenital pancreatic lipase deficiency Congenital deficiency of pancreatic lipase
	pancreatische triacylglycerollipasedeficiëntie
	deficiëntie van pancreatisch triacylglycerollipase

Id	78960005
Status	Primitive

Occurrence

Finding site

Pancreatic structure

Finding site

Gastrointestinal tract structure

DHD Diagnosis thesaurus reference set

ICD-10 complex map reference set

Target	E88.8
Rule	TRUE
Advice	ALWAYS E88.8
Correlation	SNOMED CT source code to target map code correlation not specified

Target	K90.3
Rule	TRUE
Advice	ALWAYS K90.3
Correlation	SNOMED CT source code to target map code correlation not specified